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磷酸化6丙酮酰四氫蝶呤合成酶PTPS重組兔單抗

簡要描述:The enzyme encoded by this gene catalyzes the elimination of inorganic triphosphate from dihydroneopterin triphosphate, which is the second and irreversible step in the biosynthesis of tetrahydrobiopterin from GTP. Tetrahydrobiopterin, also known as BH(4), is an essential cofactor and regulator of various enzyme activities, including enzymes involved in serotonin biosynthesis and NO synthase activity. Mutations in this gene result in hyperphenylalaninemia. [provided by RefSeq, Oct 2008]

  • 產(chǎn)品型號:bsm-62602R
  • 廠商性質(zhì):生產(chǎn)廠家
  • 更新時間:2025-03-04
  • 訪  問  量: 89

詳細(xì)介紹

Human
WB,IHC-P,IHC-F,ICC/IF,IF
Store at 4℃ for short term. Store at -20℃ for long term. Avoid repeated freeze/thaw cycles.

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